The cyclophilin inhibitor Debio 025 normalizes mitochondrial function, muslce apoptosis and ultrastructural defects in Col6a1-/- mypathic mice

T Tiepolo, A Angelin, E Palma, P Sabatelli, L Merlini, L Nicolosi, F Finetti, P Braghetta, G Vuagniaux, J-M Dumont, CT Baldari, P Bonaldo and P Bernardi

 British Journal of Pharmacology (2009)